Ebstein's anomaly
Application for Treatment
Ebstein's anomaly
This defect is rare, but can be very dangerous. Its essence lies in the fact that the tricuspid valve is shifted for some reason in the right ventricular cavity, i.e. is not in place (between the rightatrium and right ventricle), and significantly lower blood flow. Wherein the cavity of the right atrium is much higher than normal, and the right ventricle - less than normal. Flap valve itselfshifted incorrectly developed, as well as allmuscle and chordal apparatus, leading them in motion.

Children are born with Ebstein's anomaly with cyanosis that after 2-3 months may be reduced because pulmonary vascular resistance, high in the neonatal period is reduced. But if the defect in the septum is small, the condition becomes half of the children in this critical period, and they can die from increasing heart failure and complications of cyanosis in the first weeks of life. When such a flow musturgently make the procedure Rashkinda which is to increase cleft foramen ovale with the creation of a significant ASDperegorodki.Eto initially increase the amount of relief "right to left" and facilitate the work of the right heart.

However, most children do not need. Often, patients with minor anatomical changes in the heart (moderate shift valveunexpressed failure while maintaining the function of the right ventricle) and live 10-15 years, except bluish color of the skin and mucous them nothing can disturb. However, one of the most common disorders associated usually Ebstein's anomaly are various cardiac arrhythmias.

Surgery treatment of Ebstein's anomaly should eventually.

The timing of the operation is entirely dependent on the state of the child. But "favorable" within this vice is possible to postpone the operation until adolescence, of course, if there is no life-threatening complications.

Operation aims to complete the correction of vice, ie it is radical. Produce her open heart, with cardiopulmonary bypass.Excess land atrium eliminated by suturing, and the tricuspid valve with the seams lifted and strengthened in a position close to normal. If this is impossible, it is excised and replaced with an artificial prosthesis. Along the way, eliminated areas that may be sources of arrhythmias. In other words, the valve is made either plastic, or a prosthetic. Of course, the first -preferred, but prosthetics, although it has flaws, is a reliable and well established method. Unfortunately, often the choice- plastic or prosthetics - finally can be solved only on the operating table.

Esli it comes to prosthetic valve, it is better to do later, when the size of the heart is sufficient to be able to put a prosthesisdesigned for as long as possible.

Valve prostheses.

Prosthesis - an artificial valve which performs the function of a natural. It can be made of biological material (typicallyporcine valve which in size and shape corresponds to the valve fully human). It is made of fabric and heart shirts manvykraivaya of it flaps and crescent When sewing the base ring .. Mechanical valve consists entirely of titanium alloy hastwo movable sash is amazing and perfection of modern technology in medicine. These valves are designed for a long time, but steadily improved in both design and in the lineup. They are also commercially available and are used in cardiac surgery for decades.

Valve selection - mechanical or biological - is that the first is not necessary throughout life to take medication regularly,"thinning" the blood and prevent clots from forming on the valve and the second is - absolutely necessary. On the otherhand, a mechanical valve may operate for longer - for years and decades - without replacement if properly observe andmedication regimen.


Symptoms and signs of developing long-term and include:

     Fatigue, especially during exercise
     Edema of the lower extremities
     Various arrhythmias
     Discoloration of the skin and lips

Usually in neonates with Ebstein's anomaly signs of skin discoloration appear before signs of heart failure. The appearance of the above symptoms at an early age refers to a heavy defeat and requires urgent treatment.

In older age groups are determined by the signs of heart failure: fatigue, shortness of breath that occurs primarily during physical activity (games), cyanosis portion of the lips and fingertips, there are also complaints about the feeling of heaviness in the heart.

Related defects

When Ebstein's anomaly possible presence of other congenital heart defects:

More than 50 percent of the anomaly Ebshtena have a defect in the atrial septum.
Treatment on-line cost calculation